welcome to oneEDSvoice

- a positively charged Ehlers Danlos Syndrome community.
  • join today!
scientific articles

Thoracoabdominal Aortic Repair in a Patient with Ehlers-danlos Syndrome

key information

source: Annals of Thoracic Surgery

year: 2014

authors: Fukui T, Hiraoka D, Uchimuro T, Shimokawa T, Takanashi S, Takahashi Y


Type IV Ehlers-Danlos syndrome is a life-threatening inherited disorder of connective tissue associated with multiple aneurysm formation. Thoracoabdominal aortic repair in these patients has rarely been performed. We report the case of a 13-year-old patient with Ehlers-Danlos syndrome who had multiple aortic operations from the ascending aorta to the thoracoabdominal aorta.

organization: Sakakibara Heart Institute Tokyo

DOI: 10.1016/j.athoracsur.2013.08.022

read more full text source