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scientific articles

Gynecologic and Surgical Complications in Type IV Ehlers-Danlos Syndrome

key information

source: Obstetrics and Gynecology

year: 2014

authors: Wheeler SM, Russo M, Wilson-Murphy M, Shen W


Although type IV Ehlers-Danlos syndrome is a rare condition, it is critical that physicians be aware of this disease because it presents unique management challenges.
We present a young woman who was admitted with a pelvic abscess after having a miscarriage and an appendiceal perforation. She had an exploratory laparotomy secondary to a persistent pelvic abscess and endured multiple postoperative complications. Based on her family history and physical characteristics, type IV Ehlers-Danlos syndrome was diagnosed.
The decision to proceed with surgery should be weighed against tissue fragility in patients with type IV Ehlers-Danlos syndrome. A conservative, multidisciplinary team approach addresses whether to proceed with surgery and minimize postoperative complications if surgery is performed.

organization: Johns Hopkins School of Medicine

DOI: 10.1097/AOG.0000000000000001

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