welcome to oneEDSvoice
- a positively charged Ehlers Danlos Syndrome community.- join today!
- login
Ehlers–Danlos Syndrome—Hypermobility Type: A Much Neglected Multisystemic Disorder
source: Rambam Maimonides Medical Journal
year: 2016
authors: Gazit Y, Jacob G, Grahame R
summary/abstract:Ehlers–Danlos syndrome (EDS)—Hypermobility Type (HT) is considered to be the most common subtype of EDS and the least severe one; EDS-HT is considered to be identical to the joint hypermobility syndrome and manifests with musculoskeletal complaints, joint instability, and soft tissue overuse injury. Musculoskeletal complaints manifest with joint pain of non-inflammatory origin and/or spinal pain. Joint instability leads to dislocation or subluxation and involves peripheral joints as well as central joints, including the temporomandibular joints, sacroiliac joints, and hip joints. Soft tissue overuse injury may lead to tendonitis and bursitis without joint inflammation in most cases. Ehlers–Danlos syndrome-HT carries a high potential for disability due to recurrent dislocations and subluxations and chronic pain. Throughout the years, extra-articular manifestations have been described, including cardiovascular, autonomic nervous system, gastrointestinal, hematologic, ocular, gynecologic, neurologic, and psychiatric manifestations, emphasizing the multisystemic nature of EDS-HT. Unfortunately, EDS-HT is under-recognized and inadequately managed, leading to neglect of these patients, which may lead to severe disability that almost certainly could have been avoided. In this review article we will describe the known manifestations of the extra-articular systems.
organization: Tel Aviv University, Tel Aviv Sourasky Medical Center, University College LondonDOI: 10.5041/RMMJ.10261
read more full text source
expertly curated content related to this topic
-
Carotid Stiffness Change Over the Cardiac Cycle by Ultrafast Ultrasound Imaging in Healthy Volunteers and Vascular E...OBJECTIVES: Arterial stiffness is relat...
-
Ehlers-Danlos Society Receives Transformational Gift to Accelerate Genomic Research into Hypermobile EDSThe Ehlers-Danlos Society has announced ...
-
The Ehlers-Danlos Syndrome, a Disorder with Many FacesThe Ehlers-Danlos syndromes (EDSs) compr...
-
Ehlers Danlos Syndrome (Ash)Information on Ehlers-Danlos Syndrome...
-
Ehlers Danlos Syndrome (patientslikeme)We’re all in this for good. By sharing...
-
Ehlers Danlos Syndrome (Anna G.)Living with Ehlers Danlos Hypermobility ...
-
Acer Therapeutics Reports Positive Results From Pivotal Clinical Trial of EDSIVO™ (celiprolol) for Treatment of Va...Acer Therapeutics Inc., (Nasdaq:ACER), a...