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scientific articles

Cephalohematoma in a Patient with Ehlers-Danlos Syndrome

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source: Western Journal of Emergency Medicine

year: 2013

authors: Felton BM, White JM, Jones RA


Ehlers-Danlos syndrome is a rarely encountered connective tissue disorder characterized by skin hyper-elasticity, joint hyper-flexibility, and vasculature fragility. We report a 41-year-old female presenting with scalp swelling following minor head trauma. The patient presented with a large cephalohematoma that despite compressive measures and Factor IX administration continued to progress, necessitating transfer for definitive surgical intervention. The patient underwent surgical evacuation of approximately 1 liter of blood, followed by drain placement and compression dressing. This case underscores the importance for emergency physicians to recognize the potential vascular catastrophes these patients may present with following even minor injury.

organization: McLaren Greater Lansing Hospital; Michigan State University

DOI: 10.5811/westjem.2013.1.13409

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